Case report of Sleromyxedema with sensory motor axonal polyneuropathy treated with immunoglobulin therapy

---

Case Report

Author Details : Rakesh Kumar Jagdish*

Volume : 9, Issue : 1, Year : 2022

Article Page : 37-39

https://doi.org/10.18231/j.agems.2022.008

Suggest article by email

Get Permission

---

Abstract

Sleromyxedema is a rare disease characterised by extensive mucin deposition with fibrosis in dermis. It is often associated with monoclonal gammopathy. Its true prevalence and/or cause is unknown due to its rarity. Various extra-cutaneous manifestations can be associated with sleromyxedema such as dermoneuro syndrome, neuropathy, rheumatological problems or various malignancies. This case report showed that a patient with sleromyxedema and neuropathy had positive outcomes when treated with intravenous immunoglobulin (IVIg) and steroids pulses. The underlying cause of the patient’s condition was unknown.

Keywords: Sleromyxedema, Immunoglobulin therapy, Dermoneuro syndrome, Sensory Motor Axonal Polyneuropathy, Monoclonal Gannopathey

How to cite : Jagdish R K, Case report of Sleromyxedema with sensory motor axonal polyneuropathy treated with immunoglobulin therapy. Ann Geriatr Educ Med Sci 2022;9(1):37-39

This is an Open Access (OA) journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.